Atlantoaxial Rotatory Subluxation

  • Usually the subluxation leading to torticollis is persistant
  • Grisel’s syndrome
    • rotatory subluxation linked to retropharangeal inflamation of an infectious etiology
    • Usually after trivial trauma or after an URTI
  • Rarely associated with neurologic complication

Classification of Atlantoaxial Rotary Displacement

  • Feilding & Hawkins
TypeDescription
ISimple rotary displacement without anterior shift of C1
IIRotary displacement with an anterior shift of 5 mm or lessAnterior displacement of greater than 3 mm in older children & adults & greater than 4 mm in younger children is considered pathologic
IIIRotary displacement with an anterior shift greater than 5 mm
IVRotary displacement with a posterior shift
Fielding Hawkins Classification of Atlantoaxial Rotary Displacement
  • Notes
    • most common is type 1
    • Type 3 & 4 are uncommon but can lead to neurologic compromise

Clinical

  • Child usually has a crick in the neck & it lasts less than a week
  • head is laterally tilted, rotated to the other side & flexed
  • Spasm in the contralateral sternocleidomastoid
  • Rarely this becomes chronic with persistant loss of ROM
  • Neurologic compromise can occur

Differential Diagnosis

  • Congenital torticolis
  • Posterior fossa tumor
  • Ocular problem

Imaging

  • plain films may be difficult to interpret, however the mouth view may show assymetry of the lateral masses relative to the midline, the lateral may show assymetry
  • CT scan is the gold standard

Treatment

  • Mild symptoms < 1 week
    • soft collar & analgesics
  • Symptoms greater than a week & < 4 weeks
    • bedrest, halter traction, muscle relaxants & analgesia
  • If anterior displacement exists then consider careful reduction with traction followed by some form of immobilization for 6 months
  • If > 1-3 months
    • halo traction for reduction & reduction will often require later fusion
  • > 3 months
    • fixed deformity & C1 to C2 fusion is indicated

Surgical technique for Fusion

  • wiring can be used if reduction is made – Brooks or Gallie
  • in young children simply lying the bone on the decorticated C1 & C2 is adequate