Sprengel’s Deformity

  • Scapula differentiates between C4 & C6 at 5 weeks
  • Between 9-12 weeks descends to between the 2nd & 7th rib

Clinical

  • Fullness in posterior clavicular area
  • Limited abduction
  • Abnormal shape to scapula
  • Asymmetry of scapular height on x ray
  • Prescence of omovertebral bone

Associated Annomalies

  • Rotation of the scapula leaves the glenoid facing down & thus ↓ abduction
  • 25% have omovertebral bone
  • scoliosis in about 30-40%
  • diatomatomyelia, rib anomalies, abnormal muscles, torticolis
  • Klippel Feil – 24%

Presentation

  • Missing abduction
  • May be confused with Erb’s palsy due to limited abduction

General Priniples of Treatment

  • Inferior translation of the scapula
  • Resection of the superior supraspinous portion
  • Release of the omovertebral bone

Operation

  • Woodward procedure
    • Longitudinal posterior  incision from C1 to T9
    • Elevate the latisimus off of the spinous process
    • Elevate the rhomboid off the spinous process
    • Elevating this sling of muscle lateral will unroof any omohyoid bone
    • Excise omohyoid bone extra periosteal
    • Now resect the superior portion of the scapula which serves to release the levator scapulae
    • Draw the scapula down to its new level & then sew the trapezius back in place
    • Post op if there is any concern re brachia plexus – morselize the clavicle