Definition
- AKA “Brittle Bone Disease”
- Heterogeneous group of inheritable diseases
- Characterized by an abnormality of Type 1 collagen
- Manifested by bone fragility, deformity, & propensity to fracture
- Characterised by
- Bone fragility
- Deformity
- Propensity to fracture
- Ivar the Boneless (9th century)
- Scandinavian invader of England
- Carried into battle on his shield
- William the Conqueror exhumed & burnt his skeleton