Fibrosarcoma of Bone

• Presentation & localization similar to that of osteosarcoma
• occurs most often in adolescents or young adults
• presents in major long bones, presenting as painful mass
• preoperative staging studies are needed to differentiate low grade stage I fibrosarcomas from high grade stage II lesions

X-rays

• poorly defined, destructive, radiolucent lesion of metaphysis
• stage I tumors:
  • remain with in bone & have a distinct, well defined margin
• high grade tumors:
  • poorly marginated & permeative lesion with bone destruction

Treatment

• limb salvaging excision with wide margin suffices for stage Ia tumors, whereas stage IIb fibrosarcomas require radical or wide margins wtih adjuvant chemotherapy or radiation therapy
• prognosis for patients with stage II fibrosarcoma is guarded